Cystic Fibrosis

"Cystic Fibrosis" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus, MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure, which enables searching at various levels of specificity.

MeSH information

Definition | Details | More General Concepts | Related Concepts | More Specific Concepts

An autosomal recessive genetic disease of the EXOCRINE GLANDS. It is caused by mutations in the gene encoding the CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR expressed in several organs including the LUNG, the PANCREAS, the BILIARY SYSTEM, and the SWEAT GLANDS. Cystic fibrosis is characterized by epithelial secretory dysfunction associated with ductal obstruction resulting in AIRWAY OBSTRUCTION; chronic RESPIRATORY INFECTIONS; PANCREATIC INSUFFICIENCY; maldigestion; salt depletion; and HEAT PROSTRATION.

Descriptor ID	D003550
MeSH Number(s)	C06.689.202 C08.381.187 C16.320.190 C16.614.213
Concept/Terms	Cystic Fibrosis Cystic Fibrosis Fibrosis, Cystic Mucoviscidosis Pulmonary Cystic Fibrosis Pulmonary Cystic Fibrosis Cystic Fibrosis, Pulmonary Pancreatic Cystic Fibrosis Pancreatic Cystic Fibrosis Cystic Fibrosis, Pancreatic Fibrocystic Disease of Pancreas Pancreas Fibrocystic Disease Pancreas Fibrocystic Diseases Cystic Fibrosis of Pancreas

Below are MeSH descriptors whose meaning is more general than "Cystic Fibrosis".

Diseases [C]
Digestive System Diseases [C06]
Pancreatic Diseases [C06.689]
Cystic Fibrosis [C06.689.202]
Respiratory Tract Diseases [C08]
Lung Diseases [C08.381]
Cystic Fibrosis [C08.381.187]
Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16]
Genetic Diseases, Inborn [C16.320]
Cystic Fibrosis [C16.320.190]
Infant, Newborn, Diseases [C16.614]
Cystic Fibrosis [C16.614.213]

Below are MeSH descriptors whose meaning is related to "Cystic Fibrosis".

Below are MeSH descriptors whose meaning is more specific than "Cystic Fibrosis".

publications

Timeline | Most Recent

This graph shows the total number of publications written about "Cystic Fibrosis" by people in this website by year, and whether "Cystic Fibrosis" was a major or minor topic of these publications.

Bar chart showing 199 publications over 29 distinct years, with a maximum of 14 publications in 2003

To see the data from this visualization as text, click here.

Year	Major Topic	Minor Topic	Total
1991	1	0	1
1992	3	1	4
1993	0	2	2
1995	2	1	3
1996	5	0	5
1997	5	1	6
1998	5	2	7
1999	6	1	7
2000	5	0	5
2001	1	1	2
2002	6	3	9
2003	11	3	14
2004	7	0	7
2005	5	0	5
2006	5	2	7
2007	7	3	10
2008	8	2	10
2009	8	1	9
2010	7	1	8
2011	7	0	7
2012	10	1	11
2013	8	0	8
2014	8	3	11
2015	6	0	6
2016	4	1	5
2017	6	3	9
2018	5	1	6
2019	6	4	10
2020	4	1	5

Below are the most recent publications written about "Cystic Fibrosis" by people in Profiles.

Schupp JC, Khanal S, Gomez JL, Sauler M, Adams TS, Chupp GL, Yan X, Poli S, Zhao Y, Montgomery RR, Rosas IO, Dela Cruz CS, Bruscia EM, Egan ME, Kaminski N, Britto CJ. Single-Cell Transcriptional Archetypes of Airway Inflammation in Cystic Fibrosis. Am J Respir Crit Care Med. 2020 11 15; 202(10):1419-1429.

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Hou YJ, Okuda K, Edwards CE, Martinez DR, Asakura T, Dinnon KH, Kato T, Lee RE, Yount BL, Mascenik TM, Chen G, Olivier KN, Ghio A, Tse LV, Leist SR, Gralinski LE, Schäfer A, Dang H, Gilmore R, Nakano S, Sun L, Fulcher ML, Livraghi-Butrico A, Nicely NI, Cameron M, Cameron C, Kelvin DJ, de Silva A, Margolis DM, Markmann A, Bartelt L, Zumwalt R, Martinez FJ, Salvatore SP, Borczuk A, Tata PR, Sontake V, Kimple A, Jaspers I, O'Neal WK, Randell SH, Boucher RC, Baric RS. SARS-CoV-2 Reverse Genetics Reveals a Variable Infection Gradient in the Respiratory Tract. Cell. 2020 07 23; 182(2):429-446.e14.

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Zhang T, Price MB, Bravo N, Villarreal JA, Kueht ML, Vierling JM, Cotton R, Galvan T, O'Mahony CA, Goss JA, Rana A. Combined Lung-Liver and Delayed Kidney Transplantation for Cystic Fibrosis Clinical Approach and Outcome: A Case Report. Transplant Proc. 2020 Nov; 52(9):2824-2826.

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Siegel MJ, Freeman AJ, Ye W, Palermo JJ, Molleston JP, Paranjape SM, Stoll J, Leung DH, Masand P, Karmazyn B, Harned R, Ling SC, Navarro OM, Karnsakul W, Alazraki A, Schwarzenberg SJ, Seidel FG, Towbin A, Alonso EM, Nicholas JL, Murray KF, Otto RK, Sherker AH, Magee JC, Narkewicz MR. Heterogeneous Liver on Research Ultrasound Identifies Children with Cystic Fibrosis at High Risk of Advanced Liver Disease: Interim Results of a Prospective Observational Case-Controlled Study. J Pediatr. 2020 04; 219:62-69.e4.

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Hayden HS, Eng A, Pope CE, Brittnacher MJ, Vo AT, Weiss EJ, Hager KR, Martin BD, Leung DH, Heltshe SL, Borenstein E, Miller SI, Hoffman LR. Fecal dysbiosis in infants with cystic fibrosis is associated with early linear growth failure. Nat Med. 2020 02; 26(2):215-221.

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Aly FZ, Mostofizadeh S, Jawaid S. Cytological appearance of pancreatic cystosis on fine-needle aspiration. Diagn Cytopathol. 2020 Jan; 48(1):82-85.

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Ling SC, Ye W, Leung DH, Navarro OM, Weymann A, Karnsakul W, Freeman AJ, Magee JC, Narkewicz MR. Liver Ultrasound Patterns in Children With Cystic Fibrosis Correlate With Noninvasive Tests of Liver Disease. J Pediatr Gastroenterol Nutr. 2019 09; 69(3):351-357.

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Li E, Knight JM, Wu Y, Luong A, Rodriguez A, Kheradmand F, Corry DB. Airway mycosis in allergic airway disease. Adv Immunol. 2019; 142:85-140.

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Winstead RJ, Waldman G, Autry EB, Evans RA, Schadler A, Kays L, Baz M, Anstead MI, Shafii A, Goetz ME. Outcomes of Lung Transplantation for Cystic Fibrosis in the Setting of Extensively Drug-Resistant Organisms. Prog Transplant. 2019 09; 29(3):220-224.

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Steffin DHM, Hsieh EM, Rouce RH. Gene Therapy: Current Applications and Future Possibilities. Adv Pediatr. 2019 08; 66:37-54.

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