"Neurofibrosarcoma" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
A malignant tumor that arises from small cutaneous nerves, is locally aggressive, and has a potential for metastasis. Characteristic histopathologic features include proliferating atypical spindle cells with slender wavy and pointed nuclei, hypocellular areas, and areas featuring organized whorls of fibroblastic proliferation. The most common primary sites are the extremities, retroperitoneum, and trunk. These tumors tend to present in childhood, often in association with NEUROFIBROMATOSIS 1. (From DeVita et al., Cancer: Principles & Practice of Oncology, 5th ed, p1662; Mayo Clin Proc 1990 Feb;65(2):164-72)
| Descriptor ID |
D018319
|
| MeSH Number(s) |
C04.557.450.565.590.350.590 C04.557.450.795.350.590 C04.557.580.600.580.795 C10.551.775.500.750.750 C10.668.829.725.500.600.600
|
| Concept/Terms |
Neurofibrosarcoma- Neurofibrosarcoma
- Neurofibrosarcomas
- Sarcoma, Neurogenic
- Neurogenic Sarcoma
- Neurogenic Sarcomas
- Sarcomas, Neurogenic
|
Below are MeSH descriptors whose meaning is more general than "Neurofibrosarcoma".
Below are MeSH descriptors whose meaning is more specific than "Neurofibrosarcoma".
This graph shows the total number of publications written about "Neurofibrosarcoma" by people in this website by year, and whether "Neurofibrosarcoma" was a major or minor topic of these publications.
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| Year | Major Topic | Minor Topic | Total |
|---|
| 2016 | 1 | 0 | 1 |
| 2020 | 1 | 0 | 1 |
| 2021 | 1 | 0 | 1 |
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Below are the most recent publications written about "Neurofibrosarcoma" by people in Profiles.
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Not So Benign Bell's Palsy: Malignant Peripheral Nerve Sheath Tumor of the Facial Nerve Involving the Temporal Bone. J Gen Intern Med. 2021 04; 36(4):1102-1105.
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ADVL1522: A phase 2 study of lorvotuzumab mertansine (IMGN901) in children with relapsed or refractory wilms tumor, rhabdomyosarcoma, neuroblastoma, pleuropulmonary blastoma, malignant peripheral nerve sheath tumor, or synovial sarcoma-A Children's Oncology Group study. Cancer. 2020 12 15; 126(24):5303-5310.
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Malignant Peripheral Nerve Sheath Tumors in Neurofibromatosis: Impact of Family History. J Pediatr Hematol Oncol. 2018 08; 40(6):e359-e363.
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Hemisacrectomy with preservation of the contralateral sacral nerve roots and sacroiliac joint for pelvic neurofibrosarcoma in a 7-year-old child: case report with 2-year follow-up. J Neurosurg Pediatr. 2017 Jan; 19(1):102-107.