Idiopathic Pulmonary Fibrosis

"Idiopathic Pulmonary Fibrosis" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus, MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure, which enables searching at various levels of specificity.

MeSH information

Definition | Details | More General Concepts | Related Concepts | More Specific Concepts

A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

Descriptor ID	D054990
MeSH Number(s)	C08.381.483.487.500 C08.381.765.500
Concept/Terms	Idiopathic Pulmonary Fibrosis Idiopathic Pulmonary Fibrosis Idiopathic Pulmonary Fibroses Pulmonary Fibroses, Idiopathic Familial Idiopathic Pulmonary Fibrosis Fibrocystic Pulmonary Dysplasia Dysplasia, Fibrocystic Pulmonary Dysplasias, Fibrocystic Pulmonary Fibrocystic Pulmonary Dysplasias Pulmonary Dysplasia, Fibrocystic Pulmonary Dysplasias, Fibrocystic Fibrosing Alveolitis, Cryptogenic Hamman-Rich Disease Disease, Hamman-Rich Diseases, Hamman-Rich Hamman Rich Disease Hamman-Rich Diseases Interstitial Pneumonitis, Usual Interstitial Pneumonitides, Usual Pneumonitides, Usual Interstitial Pneumonitis, Usual Interstitial Usual Interstitial Pneumonitides Usual Interstitial Pneumonitis Pulmonary Fibrosis, Idiopathic Usual Interstitial Pneumonia Interstitial Pneumonia, Usual Interstitial Pneumonias, Usual Usual Interstitial Pneumonias Idiopathic Fibrosing Alveolitis, Chronic Form Cryptogenic Fibrosing Alveolitis Cryptogenic Fibrosing Alveolitides Fibrosing Alveolitides, Cryptogenic Idiopathic Pulmonary Fibrosis, Familial

Below are MeSH descriptors whose meaning is more general than "Idiopathic Pulmonary Fibrosis".

Diseases [C]
Respiratory Tract Diseases [C08]
Lung Diseases [C08.381]
Lung Diseases, Interstitial [C08.381.483]
Idiopathic Interstitial Pneumonias [C08.381.483.487]
Idiopathic Pulmonary Fibrosis [C08.381.483.487.500]
Pulmonary Fibrosis [C08.381.765]
Idiopathic Pulmonary Fibrosis [C08.381.765.500]

Below are MeSH descriptors whose meaning is related to "Idiopathic Pulmonary Fibrosis".

Below are MeSH descriptors whose meaning is more specific than "Idiopathic Pulmonary Fibrosis".

publications

Timeline | Most Recent

This graph shows the total number of publications written about "Idiopathic Pulmonary Fibrosis" by people in this website by year, and whether "Idiopathic Pulmonary Fibrosis" was a major or minor topic of these publications.

Bar chart showing 117 publications over 14 distinct years, with a maximum of 15 publications in 2021

To see the data from this visualization as text, click here.

Year	Major Topic	Minor Topic	Total
2009	2	1	3
2010	1	0	1
2011	2	1	3
2012	7	1	8
2013	7	2	9
2014	9	2	11
2015	9	0	9
2016	8	3	11
2017	12	0	12
2018	6	1	7
2019	10	0	10
2020	10	1	11
2021	14	1	15
2022	7	0	7

Below are the most recent publications written about "Idiopathic Pulmonary Fibrosis" by people in Profiles.

Wilson C, Mertens TC, Shivshankar P, Bi W, Collum SD, Wareing N, Ko J, Weng T, Naikawadi RP, Wolters PJ, Maire P, Jyothula SS, Thandavarayan RA, Ren D, Elrod ND, Wagner EJ, Huang HJ, Dickey BF, Ford HL, Karmouty-Quintana H. Sine oculis homeobox homolog 1 plays a critical role in pulmonary fibrosis. JCI Insight. 2022 May 23; 7(10).

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Kheir F, Uribe Becerra JP, Bissell B, Ghazipura M, Herman D, Hon SM, Hossain T, Khor YH, Knight SL, Kreuter M, Macrea M, Mammen MJ, Martinez FJ, Poletti V, Troy L, Raghu G, Wilson KC. Use of a Genomic Classifier in Patients with Interstitial Lung Disease: A Systematic Review and Meta-Analysis. Ann Am Thorac Soc. 2022 May; 19(5):827-832.

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Ghosh AJ, Hobbs BD, Yun JH, Saferali A, Moll M, Xu Z, Chase RP, Morrow J, Ziniti J, Sciurba F, Barwick L, Limper AH, Flaherty K, Criner G, Brown KK, Wise R, Martinez FJ, McGoldrick D, Cho MH, DeMeo DL, Silverman EK, Castaldi PJ, Hersh CP. Lung tissue shows divergent gene expression between chronic obstructive pulmonary disease and idiopathic pulmonary fibrosis. Respir Res. 2022 Apr 21; 23(1):97.

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Cottin V, Martinez FJ, Jenkins RG, Belperio JA, Kitamura H, Molina-Molina M, Tschoepe I, Coeck C, Lievens D, Costabel U. Safety and tolerability of nintedanib in patients with progressive fibrosing interstitial lung diseases: data from the randomized controlled INBUILD trial. Respir Res. 2022 Apr 07; 23(1):85.

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Westermann-Clark E, Soundararajan R, Fukumoto J, Patil SS, Stearns TM, Saji S, Czachor A, Hernandez-Cuervo H, Breitzig M, Krishnamurthy S, Lockey RF, Kolliputi N. Matrix Metalloproteinase 7 Expression and Apical Epithelial Defects in Atp8b1 Mutant Mouse Model of Pulmonary Fibrosis. Biomolecules. 2022 02 09; 12(2).

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Dubey S, Dubey PK, Umeshappa CS, Ghebre YT, Krishnamurthy P. Inhibition of RUNX1 blocks the differentiation of lung fibroblasts to myofibroblasts. J Cell Physiol. 2022 04; 237(4):2169-2182.

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de Andrade JA, Kulkarni T, Neely ML, Hellkamp AS, Case AH, Culver DA, Guntupalli K, Bender S, Conoscenti CS, Snyder LD. Associations between resources and practices of ILD centers and outcomes in patients with idiopathic pulmonary fibrosis: data from the IPF-PRO Registry. Respir Res. 2022 Jan 07; 23(1):3.

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Nakahara Y, Hashimoto N, Sakamoto K, Enomoto A, Adams TS, Yokoi T, Omote N, Poli S, Ando A, Wakahara K, Suzuki A, Inoue M, Hara A, Mizutani Y, Imaizumi K, Kawabe T, Rosas IO, Takahashi M, Kaminski N, Hasegawa Y. Fibroblasts positive for meflin have anti-fibrotic properties in pulmonary fibrosis. Eur Respir J. 2021 12; 58(6).

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Moss BJ, Ryter SW, Rosas IO. Pathogenic Mechanisms Underlying Idiopathic Pulmonary Fibrosis. Annu Rev Pathol. 2022 01 24; 17:515-546.

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de Andrade JA, Kulkarni T, Neely ML, Hellkamp AS, Case AH, Guntupalli K, Bender S, Conoscenti CS, Snyder LD. Implementation of guideline recommendations and outcomes in patients with idiopathic pulmonary fibrosis: Data from the IPF-PRO registry. Respir Med. 2021 Nov-Dec; 189:106637.

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