Atypical Hemolytic Uremic Syndrome
"Atypical Hemolytic Uremic Syndrome" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
An hereditary hemolytic uremic syndrome associated with variations in the gene that encodes COMPLEMENT FACTOR H, or the related proteins CFHR1 and CFHR3. Disease often progresses to CHRONIC KIDNEY FAILURE without the prodromal symptoms of ENTEROCOLITIS and DIARRHEA that characterize typical hemolytic uremic syndrome.
| Descriptor ID |
D065766
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| MeSH Number(s) |
C12.777.419.936.463.500 C13.351.968.419.936.463.500 C15.378.071.141.610.500 C15.378.140.855.925.500.500
|
| Concept/Terms |
Atypical Hemolytic Uremic Syndrome- Atypical Hemolytic Uremic Syndrome
- Non-Stx-Hus
- Non Stx Hus
- Non-Shiga-Like Toxin-Associated HUS
- HUS, Non-Shiga-Like Toxin-Associated
- HUSs, Non-Shiga-Like Toxin-Associated
- Non Shiga Like Toxin Associated HUS
- Non-Shiga-Like Toxin-Associated HUSs
- Toxin-Associated HUS, Non-Shiga-Like
- Toxin-Associated HUSs, Non-Shiga-Like
- Hemolytic Uremic Syndrome, Atypical
- Nonenteropathic HUS
- HUS, Nonenteropathic
- HUSs, Nonenteropathic
- Nonenteropathic HUSs
- Atypical Hemolytic-Uremic Syndrome
- Atypical Hemolytic-Uremic Syndromes
- Hemolytic-Uremic Syndrome, Atypical
- Hemolytic-Uremic Syndromes, Atypical
- Syndrome, Atypical Hemolytic-Uremic
- Syndromes, Atypical Hemolytic-Uremic
|
Below are MeSH descriptors whose meaning is more general than "Atypical Hemolytic Uremic Syndrome".
Below are MeSH descriptors whose meaning is more specific than "Atypical Hemolytic Uremic Syndrome".
This graph shows the total number of publications written about "Atypical Hemolytic Uremic Syndrome" by people in this website by year, and whether "Atypical Hemolytic Uremic Syndrome" was a major or minor topic of these publications.
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| Year | Major Topic | Minor Topic | Total |
|---|
| 2013 | 0 | 2 | 2 |
| 2014 | 0 | 2 | 2 |
| 2015 | 1 | 1 | 2 |
| 2016 | 1 | 0 | 1 |
| 2018 | 0 | 1 | 1 |
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Below are the most recent publications written about "Atypical Hemolytic Uremic Syndrome" by people in Profiles.
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Eculizumab exposure in children and young adults: indications, practice patterns, and outcomes-a Pediatric Nephrology Research Consortium study. Pediatr Nephrol. 2021 08; 36(8):2349-2360.
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Deficiency of CFHR plasma proteins and autoantibody positive hemolytic uremic syndrome: treatment rationale, outcomes, and monitoring. Pediatr Nephrol. 2021 06; 36(6):1365-1375.
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Brain microvascular endothelial cells exhibit lower activation of the alternative complement pathway than glomerular microvascular endothelial cells. J Biol Chem. 2018 05 11; 293(19):7195-7208.
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Complement activation: an atypical presentation of an atypical syndrome. BMJ Case Rep. 2017 Oct 30; 2017.
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A new therapeutic strategy for atypical HUS. Blood. 2017 07 20; 130(3):243-244.
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Atypical hemolytic uremic syndrome. Hematology Am Soc Hematol Educ Program. 2016 Dec 02; 2016(1):217-225.
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TNF Regulates Essential Alternative Complement Pathway Components and Impairs Activation of Protein C in Human Glomerular Endothelial Cells. J Immunol. 2016 Jan 15; 196(2):832-45.
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The Pharmacokinetics of Intradialytic Administration of Eculizumab in an Infant. Am J Kidney Dis. 2015 Dec; 66(6):1105-6.
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COMPLEMENTing the diagnosis of aHUS. Blood. 2014 Sep 11; 124(11):1699-700.
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Thrombotic microangiopathies and the linkage between von Willebrand factor and the alternative complement pathway. Semin Thromb Hemost. 2014 Jul; 40(5):544-50.