Gerstmann-Straussler-Scheinker Disease
"Gerstmann-Straussler-Scheinker Disease" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
An autosomal dominant familial prion disease with a wide spectrum of clinical presentations including ATAXIA, spastic paraparesis, extrapyramidal signs, and DEMENTIA. Clinical onset is in the third to sixth decade of life and the mean duration of illness prior to death is five years. Several kindreds with variable clinical and pathologic features have been described. Pathologic features include cerebral prion protein amyloidosis, and spongiform or neurofibrillary degeneration. (From Brain Pathol 1998 Jul;8(3):499-513; Brain Pathol 1995 Jan;5(1):61-75)
| Descriptor ID |
D016098
|
| MeSH Number(s) |
C10.228.228.800.350 C10.574.500.425 C10.574.843.400 C16.320.400.350
|
| Concept/Terms |
Gerstmann-Straussler-Scheinker Disease- Gerstmann-Straussler-Scheinker Disease
- Gerstmann Straussler Scheinker Disease
- Gerstmann-Straussler Inherited Spongiform Encephalopathy
- Gerstmann Straussler Inherited Spongiform Encephalopathy
- Gerstmann-Straussler Disease
- Disease, Gerstmann-Straussler
- Diseases, Gerstmann-Straussler
- Gerstmann Straussler Disease
- Gerstmann-Straussler Diseases
- Gerstmann-Straussler-Scheinker Syndrome
- Gerstmann Straussler Scheinker Syndrome
- Encephalopathy, Subacute Spongiform, Gerstmann-Straussler Type
- Gerstmann-Straussler Syndrome
- Gerstmann Straussler Syndrome
- Inherited Spongiform Encephalopathy, Gerstmann-Straussler
- Inherited Spongiform Encephalopathy, Gerstmann Straussler
|
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