Connection

HUDA ZOGHBI to Spinocerebellar Degenerations

This is a "connection" page, showing publications HUDA ZOGHBI has written about Spinocerebellar Degenerations.
Connection Strength

3.356
  1. SILencing misbehaving proteins. Nat Genet. 2005 Dec; 37(12):1302-3.
    View in: PubMed
    Score: 0.233
  2. Mutation of the E6-AP ubiquitin ligase reduces nuclear inclusion frequency while accelerating polyglutamine-induced pathology in SCA1 mice. Neuron. 1999 Dec; 24(4):879-92.
    View in: PubMed
    Score: 0.153
  3. Progress in pathogenesis studies of spinocerebellar ataxia type 1. Philos Trans R Soc Lond B Biol Sci. 1999 Jun 29; 354(1386):1079-81.
    View in: PubMed
    Score: 0.149
  4. Molecular and clinical studies in SCA-7 define a broad clinical spectrum and the infantile phenotype. Neurology. 1998 Oct; 51(4):1081-6.
    View in: PubMed
    Score: 0.142
  5. Chaperone suppression of aggregation and altered subcellular proteasome localization imply protein misfolding in SCA1. Nat Genet. 1998 Jun; 19(2):148-54.
    View in: PubMed
    Score: 0.138
  6. CAG repeats in SCA6. Anticipating new clues. Neurology. 1997 Nov; 49(5):1196-9.
    View in: PubMed
    Score: 0.133
  7. The expansion of the CAG repeat in ataxin-2 is a frequent cause of autosomal dominant spinocerebellar ataxia. Neurology. 1997 Oct; 49(4):1009-13.
    View in: PubMed
    Score: 0.132
  8. Molecular genetics and neurobiology of neurodegenerative and neurodevelopmental disorders. Pediatr Res. 1997 May; 41(5):722-6.
    View in: PubMed
    Score: 0.128
  9. The expanding world of ataxins. Nat Genet. 1996 Nov; 14(3):237-8.
    View in: PubMed
    Score: 0.124
  10. Spinocerebellar ataxia type-1 and spinobulbar muscular atrophy gene products interact with glyceraldehyde-3-phosphate dehydrogenase. Hum Mol Genet. 1996 Sep; 5(9):1311-8.
    View in: PubMed
    Score: 0.123
  11. Toward understanding polyglutamine-induced neurological disease in spinocerebellar ataxia type 1. Cold Spring Harb Symp Quant Biol. 1996; 61:649-57.
    View in: PubMed
    Score: 0.117
  12. Molecular and clinical correlations in spinocerebellar ataxia type 3 and Machado-Joseph disease. Ann Neurol. 1995 Jul; 38(1):68-72.
    View in: PubMed
    Score: 0.113
  13. Gametic and somatic tissue-specific heterogeneity of the expanded SCA1 CAG repeat in spinocerebellar ataxia type 1. Nat Genet. 1995 Jul; 10(3):344-50.
    View in: PubMed
    Score: 0.113
  14. Analysis of the CAG repeat and gene product in spinocerebellar ataxia type 1. Proc Assoc Am Physicians. 1995 Jul; 107(2):231-6.
    View in: PubMed
    Score: 0.113
  15. Expression analysis of the ataxin-1 protein in tissues from normal and spinocerebellar ataxia type 1 individuals. Nat Genet. 1995 May; 10(1):94-8.
    View in: PubMed
    Score: 0.112
  16. Spinocerebellar ataxia type 1. Semin Cell Biol. 1995 Feb; 6(1):29-35.
    View in: PubMed
    Score: 0.110
  17. Spinocerebellar ataxia type 1. Clin Neurosci. 1995; 3(1):5-11.
    View in: PubMed
    Score: 0.109
  18. Identification and characterization of the gene causing type 1 spinocerebellar ataxia. Nat Genet. 1994 Aug; 7(4):513-20.
    View in: PubMed
    Score: 0.106
  19. Mapping and cloning of the critical region for the spinocerebellar ataxia type 1 gene (SCA1) in a yeast artificial chromosome contig spanning 1.2 Mb. Genomics. 1993 Dec; 18(3):627-35.
    View in: PubMed
    Score: 0.101
  20. Expansion of an unstable trinucleotide CAG repeat in spinocerebellar ataxia type 1. Nat Genet. 1993 Jul; 4(3):221-6.
    View in: PubMed
    Score: 0.098
  21. Linkage studies in dominantly inherited ataxias. Adv Neurol. 1993; 61:133-7.
    View in: PubMed
    Score: 0.095
  22. Tight linkage of the gene for spinocerebellar ataxia to D6S89 on the short arm of chromosome 6 in a kindred for which close linkage to both HLA and F13A1 is excluded. Am J Hum Genet. 1991 Nov; 49(5):972-7.
    View in: PubMed
    Score: 0.088
  23. The gene for autosomal dominant spinocerebellar ataxia (SCA1) maps telomeric to the HLA complex and is closely linked to the D6S89 locus in three large kindreds. Am J Hum Genet. 1991 Jul; 49(1):23-30.
    View in: PubMed
    Score: 0.086
  24. Assignment of autosomal dominant spinocerebellar ataxia (SCA1) centromeric to the HLA region on the short arm of chromosome 6, using multilocus linkage analysis. Am J Hum Genet. 1989 Feb; 44(2):255-63.
    View in: PubMed
    Score: 0.072
  25. Spinocerebellar ataxia: variable age of onset and linkage to human leukocyte antigen in a large kindred. Ann Neurol. 1988 Jun; 23(6):580-4.
    View in: PubMed
    Score: 0.069
  26. Pathogenesis of polyglutamine-induced disease: A model for SCA1. Mol Genet Metab. 1999 Mar; 66(3):172-8.
    View in: PubMed
    Score: 0.036
  27. Mapping of the gene for a novel spinocerebellar ataxia with pure cerebellar signs and epilepsy. Ann Neurol. 1999 Mar; 45(3):407-11.
    View in: PubMed
    Score: 0.036
  28. Close associations between prevalences of dominantly inherited spinocerebellar ataxias with CAG-repeat expansions and frequencies of large normal CAG alleles in Japanese and Caucasian populations. Am J Hum Genet. 1998 Oct; 63(4):1060-6.
    View in: PubMed
    Score: 0.035
  29. Ataxin-1 with an expanded glutamine tract alters nuclear matrix-associated structures. Nature. 1997 Oct 30; 389(6654):971-4.
    View in: PubMed
    Score: 0.033
  30. The cerebellar leucine-rich acidic nuclear protein interacts with ataxin-1. Nature. 1997 Oct 30; 389(6654):974-8.
    View in: PubMed
    Score: 0.033
  31. Purkinje cell expression of a mutant allele of SCA1 in transgenic mice leads to disparate effects on motor behaviors, followed by a progressive cerebellar dysfunction and histological alterations. J Neurosci. 1997 Oct 01; 17(19):7385-95.
    View in: PubMed
    Score: 0.033
  32. Cloning and developmental expression analysis of the murine homolog of the spinocerebellar ataxia type 1 gene (Sca1). Hum Mol Genet. 1996 Jan; 5(1):33-40.
    View in: PubMed
    Score: 0.029
  33. SCA1 transgenic mice: a model for neurodegeneration caused by an expanded CAG trinucleotide repeat. Cell. 1995 Sep 22; 82(6):937-48.
    View in: PubMed
    Score: 0.029
  34. Retinal degeneration characterizes a spinocerebellar ataxia mapping to chromosome 3p. Nat Genet. 1995 May; 10(1):89-93.
    View in: PubMed
    Score: 0.028
  35. Neuropsychological test performance in patients with dominantly inherited spinocerebellar ataxia: relationship to ataxia severity. Neurology. 1994 Sep; 44(9):1738-46.
    View in: PubMed
    Score: 0.027
  36. Molecular genetics of hereditary ataxias. Baillieres Clin Neurol. 1994 Aug; 3(2):281-95.
    View in: PubMed
    Score: 0.027
  37. Evidence for a mechanism predisposing to intergenerational CAG repeat instability in spinocerebellar ataxia type I. Nat Genet. 1993 Nov; 5(3):254-8.
    View in: PubMed
    Score: 0.025
  38. Enhanced SUMOylation in polyglutamine diseases. Biochem Biophys Res Commun. 2002 Apr 26; 293(1):307-13.
    View in: PubMed
    Score: 0.011
  39. Interruptions in the triplet repeats of SCA1 and FRAXA reduce the propensity and complexity of slipped strand DNA (S-DNA) formation. Biochemistry. 1998 Feb 24; 37(8):2701-8.
    View in: PubMed
    Score: 0.008
  40. Mapping of the Sca1 and pcd genes on mouse chromosome 13 provides evidence that they are different genes. Genomics. 1995 Oct 10; 29(3):812-3.
    View in: PubMed
    Score: 0.007
Connection Strength

The connection strength for concepts is the sum of the scores for each matching publication.

Publication scores are based on many factors, including how long ago they were written and whether the person is a first or senior author.